Juvenile Fibromatosis: A Rare Case Report of Head and Neck Region

Abstract

Fibromatosis can be defined as a broad group of benign fibrous tissue proliferation which a has similar microscopical picture and their biological
behavior lies between benign fibrous lesions and fibrosarcoma. WHO defines fibromatosis as a tumor that originates from the mesenchymal
tissue which is nonmetastatic but presented as locally belligerent lesion which accounts for 0.03% of neoplasms and 3% of every type of soft
tissue lesions. Fibromatosis is mainly classified as superficial and deep types of fibromatosis. Superficial fibromatosis is nonaggressive, slow
growing, and does not involve deeper structures so that they are of smaller size. Deep fibromatosis is aggressive type, grows rapidly, and
penetrates extensively, whether in diffuse, multifocal, or local simulate malignancy. As it has a higher recurrence rate, the treatment of choice is
surgical excision of the lesion. Here, we present a case report of an 8-year-old male patient diagnosed as juvenile fibromatosis of the mandible
and treated surgically under general anesthesia. On 1-year follow-up, there was no recurrence of the lesion.
Keywords: Fibromatosis, Fibrosarcoma, Non metastatic.
Journal of Dental Sciences and Oral Rehabilitation (2019): 10.5005/jp-journals-10086-1208